{"created":"2023-06-19T09:12:26.948990+00:00","id":24271,"links":{},"metadata":{"_buckets":{"deposit":"2e0ee759-ea56-4995-b58c-1d6fe853b9f8"},"_deposit":{"created_by":1,"id":"24271","owners":[1],"pid":{"revision_id":0,"type":"depid","value":"24271"},"status":"published"},"_oai":{"id":"oai:kumadai.repo.nii.ac.jp:00024271","sets":["343:344:345:346"]},"author_link":["107567","107566","107565"],"item_14_alternative_title_22":{"attribute_name":"その他の言語のタイトル","attribute_value_mlt":[{"subitem_alternative_title":"Impact of liver transplantation on survival in familial amyloidotic polyneuropathy patients"}]},"item_14_alternative_title_23":{"attribute_name":"タイトル(ヨミ)","attribute_value_mlt":[{"subitem_alternative_title":"FAP ショウレイ ニ オケル セイメイ ヨゴ ニ タイスル カン イショク ノ コウカ ノ ケントウ"}]},"item_14_biblio_info_6":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2009-09-17","bibliographicIssueDateType":"Issued"},"bibliographic_titles":[{}]}]},"item_14_creator_3":{"attribute_name":"別言語の著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"Okamoto, Sadahisa"}],"nameIdentifiers":[{"nameIdentifier":"107567","nameIdentifierScheme":"WEKO"}]}]},"item_14_description_17":{"attribute_name":"フォーマット","attribute_value_mlt":[{"subitem_description":"application/pdf","subitem_description_type":"Other"}]},"item_14_description_46":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"subitem_description":"学位論文(Thesis)","subitem_description_type":"Other"}]},"item_14_description_5":{"attribute_name":"内容記述","attribute_value_mlt":[{"subitem_description":"家族性アミロイドポリニューロパチー(FAP)に対する肝移植療法は、進行を止める唯一の治療法である。FAPは進行すると栄養状態が悪化するが、良好な栄養状態で肝移植を行ったスウェーデンのFAP症例は、非移植群と比較し生存率の有意な改善を認めている。しかし、それらの肝移植症例の観察期間は中央値5年と短く、十分な解析がなされていなかった。また、発症時の年齢、性別が肝移植症例の生存率に与える影響を非移植例と比較検討した報告もない。本研究では、発症時の年齢、性別に注目し、スウェーデンにおける非移植例と肝移植例の長期生存率の比較検討を行った。","subitem_description_type":"Other"}]},"item_14_publisher_36":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"熊本大学"}]},"item_14_subject_20":{"attribute_name":"日本十進分類法","attribute_value_mlt":[{"subitem_subject":"377.5","subitem_subject_scheme":"NDC"}]},"item_14_text_18":{"attribute_name":"形態","attribute_value_mlt":[{"subitem_text_value":"7367104 bytes"}]},"item_14_text_47":{"attribute_name":"資源タイプ・ローカル","attribute_value_mlt":[{"subitem_text_value":"博士論文"}]},"item_14_text_48":{"attribute_name":"資源タイプ・NII","attribute_value_mlt":[{"subitem_text_value":"Thesis or Dissertation"}]},"item_14_text_49":{"attribute_name":"資源タイプ・DCMI","attribute_value_mlt":[{"subitem_text_value":"text"}]},"item_14_text_50":{"attribute_name":"資源タイプ・ローカル表示コード","attribute_value_mlt":[{"subitem_text_value":"03"}]},"item_14_text_81":{"attribute_name":"学位番号","attribute_value_mlt":[{"subitem_text_value":"乙博医第925号"}]},"item_14_version_type_19":{"attribute_name":"著者版フラグ","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_creator":{"attribute_name":"著者","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"岡本, 定久"}],"nameIdentifiers":[{"nameIdentifier":"107565","nameIdentifierScheme":"WEKO"}]}]},"item_files":{"attribute_name":"ファイル情報","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_date","date":[{"dateType":"Available","dateValue":"2020-03-02"}],"displaytype":"detail","filename":"32-925.pdf","filesize":[{"value":"7.4 MB"}],"format":"application/pdf","licensetype":"license_note","mimetype":"application/pdf","url":{"label":"32-925.pdf","url":"https://kumadai.repo.nii.ac.jp/record/24271/files/32-925.pdf"},"version_id":"6a610692-9da6-4b5f-8078-0f454f5192e6"}]},"item_keyword":{"attribute_name":"キーワード","attribute_value_mlt":[{"subitem_subject":"アミロイドーシス","subitem_subject_scheme":"Other"},{"subitem_subject":"家族性アミロイゴポリニューロパチー","subitem_subject_scheme":"Other"},{"subitem_subject":"FAP","subitem_subject_scheme":"Other"},{"subitem_subject":"トランスサイレチン","subitem_subject_scheme":"Other"},{"subitem_subject":"肝移植","subitem_subject_scheme":"Other"},{"subitem_subject":"生命予後","subitem_subject_scheme":"Other"}]},"item_language":{"attribute_name":"言語","attribute_value_mlt":[{"subitem_language":"jpn"}]},"item_resource_type":{"attribute_name":"資源タイプ","attribute_value_mlt":[{"resourcetype":"thesis","resourceuri":"http://purl.org/coar/resource_type/c_46ec"}]},"item_title":"FAP症例における生命予後に対する肝移植の効果の検討","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"FAP症例における生命予後に対する肝移植の効果の検討"}]},"item_type_id":"14","owner":"1","path":["346"],"pubdate":{"attribute_name":"公開日","attribute_value":"2010-12-20"},"publish_date":"2010-12-20","publish_status":"0","recid":"24271","relation_version_is_last":true,"title":["FAP症例における生命予後に対する肝移植の効果の検討"],"weko_creator_id":"1","weko_shared_id":-1},"updated":"2023-06-19T18:26:25.153693+00:00"}